KMID : 1022820140050020038
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Journal of Multiple Sclerosis and Neuroimmunology 2014 Volume.5 No. 2 p.38 ~ p.41
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A Case of Neuromyelitis Optica Spectrum Disorder Presented with HyperCKemia and Dematomyositis-like Clinical Features
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Seok Jin-Myoung
Kim Ju-Hyeon Cho Eun-Bin Cho Hye-Jin Kim Byoong-Joon Min Ju-Hong
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Abstract
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Neuromyelitis optica (NMO) is an autoimmune relapsing inflammatory disorder of the central nervous system. The detection of AQP4 antibody in NMO helped the recognition of various atypical clinical presentations including hyperCKemia. We report an anti-AQP4 antibody positive NMOSD patient presented with hyperCKemia and dematomyositis-like clinical features.
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KEYWORD
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Neuromyelitis optica, Neuromyelitis optica spectrum disorder, HyperCKemia, Aquaporin4, Dermatomyositis
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